Cystic fibrosis: management and monitoring of respiratory manifestations

An overview of the pharmacological management of respiratory symptoms in people with cystic fibrosis to ensure they can optimise benefit from their medication regime.
Young woman inhaling from nebuliser as part of cystic fibrosis treatment.

After reading this article, you should be able to:

  • Understand the pathophysiology of cystic fibrosis (CF);
  • Explain which organs are affected by CFTR dysfunction;
  • Identify the classes of drugs used to manage CFTR dysfunction and understand any considerations for efficacy or adverse effects; 
  • Understand how health in CF is monitored.  

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Peer reviewed article
This article has been peer reviewed by relevant subject experts prior to acceptance for publication. The reviewers declared no relevant affiliations or financial involvement with any organisation or entity with a financial involvement with any organisation or entity with a financial interest in or in financial conflict with the subject matter or materials discussed in this article.